Case Report
MRI Diagnosis of OHVIRA Syndrome in Adulthood: A Case Report
Achala Shravya G, Siripurapu Vinaya Ratna, Vidhya Rani R and Siddharth Pandey*
Department of Radiodiagnosis, Sapthagiri Institute of Medical Sciences and Research Centre, Bangalore, Karnataka, India
*Corresponding author:Dr. Siddharth Pandey, Department of Radiodiagnosis, Sapthagiri Institute of Medical Sciences and Research Centre, Bangalore, Karnataka, India. E-mail Id: sidd110798@gmail.com
Copyright: © 2026 Shravya GA, et al. This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
Article Information: Submission: 07/03/2026; Accepted: 27/04/2026; Published: 30/04/2026
Abstract
Obstructed hemivagina with ipsilateral renal anomaly (OHVIRA) syndrome is a rare congenital Müllerian duct anomaly. It is classically characterized by the presence of uterus didelphys, an obstructed hemivagina, and absence of the kidney on the same side (ipsilateral renal agenesis). Symptoms typically begin soon after menarche; however, delayed presentation into adulthood is very rare and may results in diagnostic confusion. Magnetic resonance imaging
(MRI) of the pelvis plays a crucial role in clearly mapping the anatomy in detail, enabling an accurate diagnosis and providing valuable guidance for surgical planning. Here we are describing a rare case of OHVIRA syndrome with a delayed presentation at 23-years of age, highlighting the MRI features which plays a crucial role in definitive diagnosis.
Keywords:OHVIRA syndrome; delayed presentation; Müllerian duct anomaly; uterus didelphys; MRI pelvis